Thoracoschisis associated with Limb Body Wall Complex.

Dragana Vujovic, Aleksandar Sretenovic, Maja Raicevic, MarijaLukac MarijaLukac, Tamara Krstajic, Vesna Ljubic, Sanja Sindjic Antunovic
Author Information
  1. Dragana Vujovic: Department of Pediatric Surgery, University Children's Hospital,Belgrade, Serbia.
  2. Aleksandar Sretenovic: Department of Pediatric Surgery, University Children's Hospital,Belgrade, Serbia.
  3. Maja Raicevic: Department of Pediatric Surgery, Clinic for Pediatric Surgery andOrthopedics, Clinical Center Nis, Nis.
  4. MarijaLukac MarijaLukac: Department of Pediatric Surgery, University Children's Hospital,Belgrade, Serbia.
  5. Tamara Krstajic: Department of Pediatric Surgery, University Children's Hospital,Belgrade, Serbia.
  6. Vesna Ljubic: Department of Neonatology, General Hospital Zemun, Belgrade, Serbia.
  7. Sanja Sindjic Antunovic: Department of Pediatric Surgery, University Children's Hospital,Belgrade, Serbia.

Abstract

Thoracoschisis is a rare condition. A female newborn presented with right-sided Thoracoschisis, associated with diaphragmatic hernia and protrusion of an accessory liver lobe through the chest wall defect along with deformity of the right forearm and hand duplication. Diagnosed as part of the limb-body wall Complex (LBWC), management included resection of the exteriorized liver lobe followed by right hemidiaphragm and thoracic wall reconstruction.

Keywords

References

  1. Genet Couns. 2006;17 (2):161-5 [PMID: 16970033]
  2. J Pediatr Surg. 1977 Oct;12(5):755-7 [PMID: 915676]
  3. Am J Med Genet. 1992 Jul 15;43(5):780-4 [PMID: 1642261]
  4. European J Pediatr Surg Rep. 2015 Jun;3(1):40-2 [PMID: 26171314]
  5. J Pediatr Surg. 2011 Nov;46(11):2181-3 [PMID: 22075354]
  6. Fetal Pediatr Pathol. 2015;34(5):307-14 [PMID: 26207297]
  7. Am J Med Genet. 1987 Nov;28(3):529-48 [PMID: 2962493]
  8. Indian J Pediatr. 2004 Mar;71(3):265-7 [PMID: 15080415]
  9. Turk J Pediatr. 2001 Jul-Sep;43(3):269-71 [PMID: 11592524]
  10. Indian Pediatr. 2003 Sep;40(9):891-4 [PMID: 14530552]
  11. J Indian Assoc Pediatr Surg. 2012 Apr;17(2):78-9 [PMID: 22529555]