Esthesioneuroblastoma Presenting with Bilateral Proptosis and Blindness in a Child: A Case Report.

Mahdi Shahriari, Nader Shakibazad, Mehrpour Moradi
Author Information
  1. Mahdi Shahriari: Associate Professor, Department of Paediatrics, Division of Paediatric Haematology and Oncology, Shiraz University of Medical Sciences, Shiraz, Fars, Iran.
  2. Nader Shakibazad: Paediatric Oncology and Haematology Fellow, Department of Paediatrics, Division of Paediatric Haematology and Oncology, Shiraz University of Medical Sciences, Shiraz, Fars, Iran.
  3. Mehrpour Moradi: Paediatric Oncology and Haematology Fellow, Department of Paediatrics, Division of Paediatric Haematology and Oncology, Shiraz University of Medical Sciences, Shiraz, Fars, Iran.

Abstract

Esthesioneuroblastoma is a rare malignant tumour of the olfactory epithelium. The most common symptom is related to unilateral nasal obstruction. It rarely presents with bilateral proptosis and blindness. We report a 21-month-old girl with esthesioneuroblastoma in sphenoid and ethmoid sinus in a child presenting with bilateral proptosis, blindness, and irritability. The diagnosis was confirmed by histopathology.

Keywords

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Word Cloud

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