Olfactory Neuroblastoma: An Unusual Ocular Presentation.

Dhabiah Saeed AlQahtani, Abdulaziz A Alshamrani, Raniah AlQawahmed, Sahar Elkhamary, Huda AlGhadeer
Author Information
  1. Dhabiah Saeed AlQahtani: Ophthalmology Department, King Khaled Eye Specialist Hospital, Riyadh, Kingdom of Saudi Arabia.
  2. Abdulaziz A Alshamrani: Ophthalmology Department, King Khaled Eye Specialist Hospital, Riyadh, Kingdom of Saudi Arabia.
  3. Raniah AlQawahmed: Pathology Department, Prince Sultan Military Medical City, Riyadh, Kingdom of Saudi Arabia.
  4. Sahar Elkhamary: Radiology Department, King Khaled Eye Specialist Hospital, Riyadh, Saudi Arabia.
  5. Huda AlGhadeer: Emergency Department, King Khaled Eye Specialist Hospital, Riyadh, Kingdom of Saudi Arabia. ORCID

Abstract

We report a case of 51-year-old medically healthy male who presented with gradual painless diminution of vision in both eyes for 3 months. His visual acuity was hand movement perception in the right eye, and no light perception in the left eye. The intraocular pressure, external eye examination, ocular motility and anterior segment examinations were normal. Fundus examination revealed severe bilateral papilloedema and engorged tortuous veins in both eyes. Imaging exhibited a large intracranial tumour causing raised intracranial pressure. This was debulked by neurosurgery and histological examination revealed that the tumour was an olfactory neuroblastoma (ONB). This case is noteworthy since ONBs rarely present with isolated papilloedema without any accompanying ophthalmoplegia, proptosis, epistaxis, nasal, or neurological symptoms.

Keywords

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