Transcatheter Closure of Superior Sinus Venosus Defects.

Alban-Elouen Baruteau, Sébastien Hascoet, Sophie Malekzadeh-Milani, Clément Batteux, Clément Karsenty, Vlad Ciobotaru, Jean-Benoit Thambo, Alain Fraisse, Younes Boudjemline, Zakaria Jalal
Author Information
  1. Alban-Elouen Baruteau: Nantes Université, Centre Hospitalier Universitaire Nantes, Department of Pediatric Cardiology and Pediatric Cardiac Surgery, Nantes, France; Nantes Université, Centre Hospitalier Universitaire Nantes, Centre National de la Recherche Scientifique, Institut National de la Santé et de la Recherche Scientifique, l'institut du thorax, Nantes, France; Nantes Université, Centre Hospitalier Universitaire Nantes, Institut National de la Santé et de la Recherche Scientifique, Centre d'Investigations Cliniques Femmes-Enfants-Adolescents 1413, Nantes, France; Nantes Université, Institut National de Recherche pour l'Agriculture, l'Alimentation et l'Environnement, Unité Mixte de Recherche 1280, Physiologie des Adaptations Nutritionnelles, Nantes, France. Electronic address: albanelouen.baruteau@chu-nantes.fr.
  2. Sébastien Hascoet: Malformations Cardiaques Congénitales Complexes-Hôpital Marie Lannelongue, Department of Pediatric Cardiology and Congenital Heart Disease, Groupe Hospitalier Paris Saint Joseph, BME Lab, Institut National de la Santé et de la Recherche Scientifique UMR-S 999, Université Parsis Saclay, Le Plessis Robinson, France.
  3. Sophie Malekzadeh-Milani: Malformations Cardiaques Congénitales Complexes-Necker, Department of Congenital and Pediatric Cardiology, Hôpital Necker-Enfants Malades, Assistance Publique Hôpitaux de Paris, Université de Paris, Paris, France.
  4. Clément Batteux: Malformations Cardiaques Congénitales Complexes-Hôpital Marie Lannelongue, Department of Pediatric Cardiology and Congenital Heart Disease, Groupe Hospitalier Paris Saint Joseph, BME Lab, Institut National de la Santé et de la Recherche Scientifique UMR-S 999, Université Parsis Saclay, Le Plessis Robinson, France.
  5. Clément Karsenty: Department of Pediatrics, Centre Hospitalier Universitaire Toulouse, Université de Toulouse, Toulouse, France; Institut des Maladies Métaboliques et Cardiovasculaires, Université de Toulouse, Toulouse, France.
  6. Vlad Ciobotaru: Malformations Cardiaques Congénitales Complexes-Hôpital Marie Lannelongue, Department of Pediatric Cardiology and Congenital Heart Disease, Groupe Hospitalier Paris Saint Joseph, BME Lab, Institut National de la Santé et de la Recherche Scientifique UMR-S 999, Université Parsis Saclay, Le Plessis Robinson, France; Clinique des Franciscaines, 3Dheartmodeling, Nîmes, France.
  7. Jean-Benoit Thambo: Department of Pediatric and Adult Congenital Cardiology, Centre Hospitalier Universitaire Bordeaux, Bordeaux, France; Electrophysiology and Heart Modeling Institute, Institut Hospital-Universitaire Liryc, Fondation Bordeaux Université, Bordeaux, France.
  8. Alain Fraisse: National Heart and Lung Institute, Imperial College London, Royal Brompton and Harefield Hospitals, London, United Kingdom.
  9. Younes Boudjemline: Sidra Heart Center, Sidra Medicine, Weil Cornell Medical College, Doha, Qatar.
  10. Zakaria Jalal: Department of Pediatric and Adult Congenital Cardiology, Centre Hospitalier Universitaire Bordeaux, Bordeaux, France; Electrophysiology and Heart Modeling Institute, Institut Hospital-Universitaire Liryc, Fondation Bordeaux Université, Bordeaux, France.

Abstract

Superior sinus venosus defect is a communication between the right and left atrium located above the upper margin of the oval fossa, immediately inferior to the junction of the superior vena cava and the right atrium. It is systematically associated with partial anomalous pulmonary venous drainage, especially of the right upper pulmonary vein. Surgical repair has been the gold standard approach to close that defect. Introduced in 2014, percutaneous closure has gradually become a safe and effective alternative to surgery in carefully selected patients, although worldwide experience remains limited. This article provides an appraisal of the patients' selection process and a step-by-step description of the procedure as well as a comprehensive review of its outcomes.

Keywords

MeSH Term

Humans
Vena Cava, Superior
Treatment Outcome
Heart Septal Defects, Atrial
Pulmonary Veins

Word Cloud

Created with Highcharts 10.0.0defectrightsinusvenosusatriumupperpulmonaryclosureSuperiorcommunicationleftlocatedmarginovalfossaimmediatelyinferiorjunctionsuperiorvenacavasystematicallyassociatedpartialanomalousvenousdrainageespeciallyveinSurgicalrepairgoldstandardapproachcloseIntroduced2014percutaneousgraduallybecomesafeeffectivealternativesurgerycarefullyselectedpatientsalthoughworldwideexperienceremainslimitedarticleprovidesappraisalpatients'selectionprocessstep-by-stepdescriptionprocedurewellcomprehensivereviewoutcomesTranscatheterClosureSuperior Sinus VenosusDefects3-dimensionaltechnologycongenitalheartdiseasemultimodalfusionimagingtranscatheter

Similar Articles

Cited By