General anaesthesia in a child with Larsen syndrome.

L A H Critchley, L Chan
Author Information
  1. L A H Critchley: Department of Anaesthesia and Intensive Care, Chinese University of Hong Kong, Prince of Wales Hospital, Shatin, New Territories, Hong Kong, China.

Abstract

Larsen syndrome is a rare congenital connective tissue disorder which is characterized by multiple dislocations of major joints, typical facial appearance, cervical spine narrowing and instability and respiratory difficulties secondary to laryngotracheomalacia. A case of general anaesthesia for laparoscopic hernia repair in a male child aged 16 months with this syndrome is presented. Anaesthesia was well tolerated though intubation proved difficult. Cervical spine instability and postoperative respiratory complications are potential problems.

MeSH Term

Anesthesia, General
Anesthetics, Intravenous
Connective Tissue Diseases
Fentanyl
Hernia, Inguinal
Humans
Infant
Laparoscopy
Male

Chemicals

Anesthetics, Intravenous
Fentanyl

Word Cloud

Created with Highcharts 10.0.0syndromeLarsenspineinstabilityrespiratoryanaesthesiachildrarecongenitalconnectivetissuedisordercharacterizedmultipledislocationsmajorjointstypicalfacialappearancecervicalnarrowingdifficultiessecondarylaryngotracheomalaciacasegenerallaparoscopicherniarepairmaleaged16monthspresentedAnaesthesiawelltoleratedthoughintubationproveddifficultCervicalpostoperativecomplicationspotentialproblemsGeneral

Similar Articles

Cited By (3)